NEONATAL BOWEL OBSTRUCTION
Transcription
NEONATAL BOWEL OBSTRUCTION
NEONATAL BOWEL OBSTRUCTION Humberto Lugo-Vicente MD FACS FAAP Professor Pediatric Surgery UPR School of Medicine NEONATE FAILURE TO PASS MECONIUM BILIOUS VOMITING ABDOMINAL DISTENSION PYLORIC, DUODENAL or JEJUNAL atresia/stenosis NEC SIMPLE ABDOMINAL FILMS dilated bowel loops dilated bowel loops with calcifications, gasless abdomen with eggshell calcification CONTRAST ENEMA microcolon Air-fluid levels NO microcolon NO air-fluid levels ground-glass appearance MECONIUM PERITONITIS GIANT CYSTIC MECONIUM PERITONITIS Transitional zone barium retention past 24 hours MECONIUM PLUG SYNDROME INTESTINAL ATRESIA HYPOPERISTALSIS SYNDROME MECONIUM ILEUS Rectal biopsy HIRSCHSPRUNG’S LEFT HYPOPLASTIC COLON Congenital bowel obstruction • Triad – Bilious vomiting – Retained meconium – Abdominal distension • Pathologic types – Intraluminal – Extraluminal – Functional • Aids in early dx – Mother history, miscarriage, siblings – Polyhydramnious • Investigation – Plain X-ray (KUB or babygram) – Contrast studies (enema or UGIS) Gastro-pyloric anomalies • Pyloric atresia – Epidermolysis bullosa – Management • gastroduodenostomy • Pyloric stenosis Pyloric stenosis • • • • • • • Concentric muscle hypertrophy Males:female 4:1 Post-prandial non-bilious vomiting Metabolic hypochloremic alkalosis Dehydration Palpable pyloric muscle Diagnosis – US – UGIS • Management – hydration – Pyloromyotomy – Periumbilical approach Duodenal lesions • Bilious vomiting • Types – – – – Atresia Stenosis Annular pancreas Ladd’s bands • Diagnosis – KUB – Colon contrast study • Associated anomalies – Cardiac – Down’s syndrome Duodenal atresia • KUB – Double bubble • Down’ syndrome – 30% • Management – Duodenoduodenostomy Case 1 5 days-old-male with intermittent bilious vomiting and no abdominal distension. Meconium passed at birth. Duodenal stenosis • KUB – Double-bubble – Scanty air distally • Causes – Pure stenosis – Annular pancreas – Ladd’s bands • Management – Depends on cause Case 2 10 days well-baby develops abdominal distension, bilious vomiting and metabolic acidosis Malrotation and Volvulus • Embryology – Clockwise rotation midgut – Obstruction 3rd portion duodenum – Ischemia midgut • Symptoms – Bilious vomiting – Abdominal distension – Metabolic acidosis • Diagnosis – KUB – UGIS – contrast enema • Management – Ladd’s procedure – Laparoscopic Malrotation: Embryology Volvulus: Dx • Diagnosis – UGIS – Contrast enema Volvulus: Tx • Ladd’s procedure – Counter-clockwise derotation bowel – Lysis Ladd’s bands – Incidental appendectomy Case 3 2 days-old baby-girl with bilious vomiting, obstipation and no abdominal distension Intestinal atresias • Intrauterine vascular accident • Types • Diagnosis – Bilious vomiting – Abdominal distension • KUB – Dilated bowel loops • Contrast enema – Microcolon • Management – anastomosis Meconium Diseases • Meconium peritonitis • Meconium ileus • Meconium plug syndrome Meconium Peritonitis • Intrauterine bowel perforation • Types – Simple • observe – Complicated • Resection/anastomosis or enterostomy • KUB – Calcifications • Associated – Cystic fibrosis Case 4 2 days-old-female with bilious vomiting, abdominal distension, no passage of meconium. Colon contrast: microcolon with intraluminal meconium pellets Meconium Ileus • Intraluminal obstruction • Cystic fibrosis • Types – Simple – Complicated • KUB – Multiple dilated bowel loops – “water-soap” appearance • Management – Medical • Gastrograffin enema • Pancreatic enzyme replacement – Surgical • Enterostomy • evacuation Meconium plug syndrome • Grey impacted meconium • Distal obstruction • Remove manually • R/O – aganglionosis Case 5 2 days-old full-term male with abdominal distension and no passage of meconium or Hirschsprung’s Disease • • • Congenital absence ganglion cells Absent cranio-caudal migration neuroblast Symptoms – Absent meconium 1st 48 hrs of life – Painless abdominal distension – TAGA male • Diagnosis – First enema: barium enema – Suction rectal biopsy • Management – Laparoscopic Pull-through – Neonatal > 5 kg weight – Colostomy • • • • Perforated HAEC Premature No compliance Imperforate Anus • Physical exam • Males vs female defect • Associated anomalies – Cardiac – Renal • Management – anoplasty – Initial colostomy – PSARP Bowel Duplications • • • • Rare Distal ileum Cystic or tubular Management – Resection – anastomosis NEC: Bells’ Classification • Stage 1: Suspect – Perinatal asphyxia, abd distension, blood in stools, gastric residue, ileus in KUB • Stage 2: Definitive – Cellulitis, edema, pneumatosis – Thrombocytopenia, metabolic acidosis – Portal vein air • Stage 3: Advance – Pneumoperitoneum – Intractable metabolic acidosis NEC: Initial Tx • Volume replacement • Respiratory support • Correct electrolytes/ABG • Antibiotherapy • Stop feedings • Monitor – CBC, SMA-6 • KUB (cross-table) NEC: Surgical principles • Drain, patch & wait • Resect gangrenous bowel • Avoid massive resections • Exteriorize bowel